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  • ACOX1 抗原(重組蛋白)

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    • 品牌 : 通蔚生物
    • 目錄號 : TW15723
    • 應用 : 僅供科研使用
    • 貨期 : 現(xiàn)貨
    • 規(guī)格 :100ug
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中文名稱:ACOX1 抗原(重組蛋白)

英文名稱: ACOX1 Antigen (Recombinant Protein)

別      名: Acyl-CoA oxidase 1, palmitoyl; ACOX; SCOX; PALMCOX

儲      存: 冷凍(-20℃)

相關類別: 抗原

概  述:

Fusion protein corresponding to C terminal 250 amino acids of human ACOX1


技術規(guī)格:

Full name:

Acyl-CoA oxidase 1, palmitoyl

Synonyms:

ACOX; SCOX; PALMCOX

Swissprot:

Q15067

Gene Accession:

BC010425

Purity:

>85%, as determined by Coomassie blue stained SDS-PAGE

Expression system:

Escherichia coli

Tags:

His tag C-Terminus, GST tag N-Terminus

Background:

The protein encoded by this gene is the first enzyme of the fatty acid beta-oxidation pathway, which catalyzes the desaturation of acyl-CoAs to 2-trans-enoyl-CoAs. It donates electrons directly to molecular oxygen, thereby producing hydrogen peroxide. Defects in this gene result in pseudoneonatal adrenoleukodystrophy, a disease that is characterized by accumulation of very long chain fatty acids. Alternatively spliced transcript variants encoding different isoforms have been identified.



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